FaCD Online Syndrome Fact Sheet
Last updated: 21 Feb 2008
Name: Dermatofibrosarcoma Protuberans, Familial Clustering of
Mode of Inheritance: multifact/ AD?
Tumor featuresdermatofibrosarcoma protuberans
Comment
Gardner et al[1] reported a father and son with a dermatofibrosarcoma protuberans, a locally aggressive cutaneous tumor of probably fibroblastic origin, at the age of 44 and 21 years, respectively.
References
[1] Gardner TL, Elston DM, Wotowic PJ. A familial dermatofibrosarcoma protuberans. J Am Acad Dermatol 39[3], 504-505. 1998.
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