FaCD Online Syndrome Fact Sheet

Last updated: 21 Feb 2008

Name: Dermatofibrosarcoma Protuberans, Familial Clustering of

Mode of Inheritance: multifact/ AD?

Tumor features

dermatofibrosarcoma protuberans

Comment

Gardner et al[1] reported a father and son with a dermatofibrosarcoma protuberans, a locally aggressive cutaneous tumor of probably fibroblastic origin, at the age of 44 and 21 years, respectively.

References

[1] Gardner TL, Elston DM, Wotowic PJ. A familial dermatofibrosarcoma protuberans. J Am Acad Dermatol 39[3], 504-505. 1998.